Ossifying fibroma of the maxilla and tuberous sclerosis complex.

A 19-year-old man with refractory generalized epilepsy related to tuberous sclerosis complex (TSC) (figure 1) complained of chronic left facial swelling. Physical examination disclosed typical mucocutaneous findings of TSC (hypomelanotic macules, shagreen patch, ungual fibromas, facial angiofibromas) and a hardened well-limited mass in his left maxilla, evidenced as an odontogenic extensive left maxillary mass (figure 2). Histopathologic study was compatible with an ossifying fibroma. TSC is a major neurocutaneous syndrome frequently associated with gingival hyperplasia or fibromas. Ossifying maxillary fibroma is an extremely rare finding associated with TSC.